Hurler Syndrome
People with Hurler syndrome often develop hepatosplenomegaly, an enlargement
of the liver and spleen caused by GAG accumulation in these organs.
The large size of the liver and spleen may interfere with eating and
breathing, due to crowding of the stomach and lungs.
Hernias (protrusion of the abdominal organs through a weakened area
of the abdominal muscles) are common in Hurler syndrome. The hernia
may come from behind the belly button (umbilical hernia) or in the groin
(inguinal hernia). Hernias may be repaired with surgery. They may recur
after they are repaired.
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